Congenital Lobar Emphysema

  • Etiology: intrinsic airway obstruction due to cartilage abnormality or extrinsic airway compression leading to congenital ball valve effect
  • CXR: single large lesion with retention of fluid at birth and air trapping later
  • Imaging: Usually affects upper lobes (left upper lobe > right middle lobe > right upper lobe > lower lobes)

Cases of Congenital Lobar Emphysema

CXR of congenital lobar emphysema
CXR on day 1 (above) shows a semi-solid mass in the right middle lobe obscuring the right heart border. CXR on day 5 (below) shows the right middle lobe mass has now cleared of fluid and has filled with air and is causing mediastinal shift to the left.