Prune Belly Syndrome

  • Etiology: triad is hypoplastic abdominal wall musculature / urinary tract dilation (but not obstructed) / cryptorchidism
  • VCUG: dilated posterior urethra, trabeculated thick walled bladder, bilateral hydroureteronephrosis from vesicoureteral reflux -> renal damage so kidneys can be small + echogenic on US
  • Clinical: pulmonary hypoplasia due to oligohydramnios, patent urachus helps to decompress, hydroureteronephrosis + bladder distension leads to flank masses

Radiology Cases of Prune Belly Syndrome

AXR of peripherally inserted central catheter / PICC in the renal vein in a patient with gastroschisis
AXR AP and lateral shows a right lower extremity PICC coursing across the midline with its tip projecting over the left renal vein. The abdomen appears to be bulging and protruberant in both medial-lateral and anterior-posterior dimensions. The tip of the bladder catheter projects high within the pelvis within a dilated bladder

Clinical Cases of Prune Belly Syndrome

Clinical image of prune belly syndrome / Eagle Barrett syndrome
Clinical image shows a small thorax, a bulging abdomen due to hypoplastic abdominal wall musculature, and bilateral undescended testicles.