- Etiology: Can occur within the ventricle (infundibular stenosis) or at pulmonary valve (valvular stenosis) or in pulmonary artery (peripheral stenosis), isolated valvular stenosis is much more common, can occur by itself or in complex isolated valvular stenosis, due to fusion of 3 cusps of the valve
- CXR: Post stenotic dilation of main pulmonary artery especially in left pulmonary artery because jet of blood shoots straight into it, heart is normal is size as is the pulmonary vascularity, right ventricular hypertrophy does not change the size of right ventricle but an upturned cardiac apex can be seen due to superior displacement of the left ventricle by the hypertrophied right ventricle
- DDX:
- Complications: Stenosis leads to increased right ventricle end systolic pressure and right ventricular hypertrophy and then right ventricular dilation when the right ventricle decompensates
- Treatment:
- Clinical: Usually asymptomatic with a systolic thrill associated with an ejection type murmur heard best over pulmonary area
Radiology Cases of Pulmonary Stenosis
Radiology Cases of Valvular Pulmonary Stenosis
![CXR and angiogram of valvular pulmonary stenosis](https://pediatricimaging.org/wp-content/uploads/2024/06/pulmonarystenosis01jakcxrangio.jpg?w=1100)
Radiology Cases of Peripheral Pulmonary Stenosis of the Left Pulmonary Artery
![CXR of left pulmonary artery stenosis](https://pediatricimaging.org/wp-content/uploads/2024/06/pulmonaryarterystenosis02jakleftpulmonaryarterycxr2yo.jpg?w=1100)