Pediatric Angiomyolipoma

  • Etiology: Hamartoma containing fat
  • Imaging:
    — Fat containing renal lesion
    — Often multiple
  • DDX:
  • Complications:
  • Treatment:
  • Clinical: Seen in tuberous sclerosis

Radiology Cases of Angiomyolipoma

Radiology Cases of Angiomyolipoma With Macroscopic Fat

Axial CT without contrast of the abdomen shows the right kidney to be normal in size and to contain multiple small low density lesions that when measured demonstrate negative Hounsfield units. The left kidney, which is massively enlarged, also contains multiple small low density lesions as well as one extremely large low density lesion in its anterior aspect.
MRI of renal angiomyolipomas in a patient with tuberous sclerosis.
Axial T1 MRI without contrast of the abdomen shows two oval hyperintense lesions in the right kidney that have similar signal intensity to the subcutaneous fat. No renal cysts were seen.

Radiology Cases of Angiomyolipoma With Macroscopic Fat and Microscopic Fat

CT of angiomyolipomas
Axial CT with contrast of the abdomen shows a small round low density lesion in the posterolateral aspect of the left kidney (above) and a larger round low density lesion in the posterior aspect of the right kidney (below). There is also an intermediate density round lesion in the anteromedial aspect of the left kidney (above).