Pediatric Atretic Cephalocele

  • Etiology:
    — Cephalocele = extracranially-herniated intracranial tissue
    — Involution of true encephalocele
  • Imaging:
    — Typically parietal in location (or occipital)
    — Persistent falcine sinus common
    — Fibrous stalk at base connects to dura
    — Contains meninges and fibrous tissue and dysplastic brain tissue
  • DDX:
  • Complications:
  • Treatment: Surgical
  • Clinical:

Radiology Cases of Atretic Cephalocele

MRI of atretic cephalocele
Sagittal T2 (above left) and sagital CISS (above right) MRI without contrast of the brain shows a fluid filled parietal lesion that contains meninges and that is connected by a short stalk to the dura. A persistent falcine sinus is present. Axial T2 MRI (below) shows the lesion to be in the midline.
MRI of atretic cephalocele
Sagittal T2 MRI of the brain shows in the subcutaneous tissue at the vertex of the skull a subgaleal lipomatis and cystic lesion in close approximation to a persistent falcine sinus.