- Etiology: microcystic disease occurring in the distal convoluted tubules and collecting ducts
- US: bilateral enlarged / echogenic / nonfunctioning kidneys, may also have hepatic fibrosis and intra + extrahepatic biliary dilation with there being an inverse relationship between hepatic + renal involvement, individual renal microcyts may be difficult to resolve
- Clinical: may present with oligohydramnios, pulmonary hypoplasia, respiratory failure
Radiology Cases of Autosomal Recessive Polycystic Kidney Disease
