AV Canal

  • Etiology: spectrum of ostium primum atrial septal defect, cleft mitral leaflet, inlet ventricular septal defect, common AV valve, complete endocardial cushion defect
  • CXR: Shunt vascularity, cardiomegaly, gooseneck deformity = elongation of left ventricular outflow tract on angiogram
  • Clinical: 30% of AV canal seen in Down syndrome, 30% of Down syndrome have AV canal

Cases of AV Canal

CXR of AV canal / endocardial cushion defect
CXR AP and lateral shows hyperexpanded lungs, increased pulmonary vascularity and marked cardiomegaly.