Pediatric Cystic Fibrosis Pancreas

  • Etiology: pancreatic insufficiency -> fatty atrophy
  • Imaging: variable appearance of pancreas from totally fatty replaced to small and fibrotic, can see macrocysts and calcifications
  • Clinical: most common cause of pancreatic insufficiency in children

Radiology Cases of Cystic Fibrosis Pancreas

AXR of cystic fibrosis with pancreatic insufficiency
AXR shows calcifications throughout the pancreas.