Ebstein Anomaly

  • Etiology: enlarged right atrium + atrialization of right ventricle due to downwardly displaced tricuspid valve
  • CXR: box-shaped heart / wall to wall heart, decreased pulmonary artery pattern = oligemic lung

Cases of Ebstein Anomaly

CXR of Ebstein anomaly
CXR AP shows decreased pulmonary vascularity and a huge box-shaped heart.