- Etiology: tumor of cartilage rests deposited in medullary cavity as growth plate moves away from diaphysis
- Imaging: multiple enchondromas + hemangiomas / lymphangiomas, asymmetric involvement
- Complications: chondrofibrosarcoma in 30%, associated with CNS / ovarian / pancreatic malignancy
Radiology Cases of Enchondromatosis – Maffucci Syndrome
