Pediatric Epithelioid Sarcoma

  • Etiology: High grade soft tissue tumor
  • Imaging: Soft tissue mass with variable appearance
  • DDX:
  • Complications: Metastasize most commonly to lymph nodes and lungs
  • Treatment:
  • Clinical: May present as a non-healing skin ulcer

Radiology Cases of Epithelioid Sarcoma

CT of epithelioid sarcoma with pulmonary metastases
Axial CT without contrast of the chest with soft tissue (above) and lung (below) windows shows a heterogeneous mass contiguous with the rectus muscles and anterior to the lower sternum which appears to be eroding into the sternum along with multiple peripheral pulmonary soft tissue nodules.