Pediatric Fibromatosis

  • Etiology: Benign but locally aggressive
  • Imaging:
    — Located at base of mesentery and surrounds vessels and bowel
    — Imaging appearance depends on content of collagen versus myxoid change and degree of cellularity and vascularity
    — Presence of fluid signal may predict growth on followup
    — Increased vascularity predicts growth on followup
  • Imaging MRI:
    — T1WI: Hypointense to isointense to muscle
    — T1WI post contrast: Mild and heterogenous enhancement
    — T2WI: Variable intensity to muscle
  • DDX:
  • Complications:
  • Treatment:
  • Clinical: Associated with Gardener syndrome

Radiology Cases of Fibromatosis

CT of fibromatosis
Axial (above), coronal (below left) and sagittal (below right) CT with contrast of the abdomen show a round, avidly enhancing soft tissue mass arising from the subcutaneous tissues to the left of midline.