A Pediatric Radiology Textbook and Pediatric Radiology Digital Library
Pediatric Fibrosarcoma
Etiology:
Imaging: — Location: Metaphysis — Lytic or blastic: Lytic — Matrix: Fibrous — Zone of transition: Wide — Periosteal New bone or cortical destruction: Cortical destruction present — Additionally: Usually associated with soft tissue mass extending from bone
DDX:
Complications:
Treatment: Surgical
Clinical:
Radiology Cases of Fibrosarcoma
Radiology Cases of Fibrosarcoma of the Bone
AP (left) and lateral (right) radiographs of the tibia and fibula show in the tibia a metaphyseal lesion that is lytic in appearance with a fibrous matrix and a wide zone of transition with cortical destruction and faint periosteal reaction.
Radiology Cases of Fibrosarcoma of the Abdomen
Coronal (above left) T2 MRI of the abdomen shows a right-sided heterogenous and hyperintense oval shaped suprarenal retroperitoneal mass that on sagittal T2 MRI (above right) is anterior to the spine (which has an incidental segmentation anomaly at T10-T12) and which on axial T2 MRI (below left) is seen to cross the midline in close proximity to the inferior vena cava and aorta. On axial T1 MRI with contrast (below right) the mass shows some enhancement. Other imaging (not provided) revealed invasion of the inferior vena cava by the mass and lung metastases.