A Pediatric Radiology Textbook and Pediatric Radiology Digital Library
Gaucher Disease
Etiology: Lysosomal storage disease
Imaging Radiograph: Erlenmeyer flask deformity on femoral radiographs with reduced constriction of diaphysis and flaring of metaphysis due to undertubulation
DDX:
Complications:
Treatment:
Clinical:
Radiology Cases of Gaucher Disease
Coronal T1 MRI without contrast (left) and T2 MRI (right) of the femurs shows a heterogeneous appearance to the bone marrow of the femurs due to diffuse marrow infiltration. The femurs have a mildly reduced constriction of diaphysis and flaring of metaphysis due to undertubulation, giving them the appearance of an Erhlemeyer flask.Coronal T1 MRI without contrast (left) and coronal T2 MRI (right) of the femurs shows a heterogeneous appearance to the bone marrow of the femurs due to diffuse marrow infiltration. The femurs have a mildly reduced constriction of diaphysis and flaring of metaphysis due to undertubulation, giving them the appearance of an Erhlemeyer flask.