Imaging: — 70-80% solitary — Range 1-15 centimeters in size — Multiple lesions common in patients with glycogen storage disease or liver adenomatosis — Hepatic adenomatosis (greater than 9 hepatic adenomas)
Imaging CT: — Well defined mass that can contain hemorrhage, necrosis, fat and rarely calcification — Non contrast: Hypodense or isodense — Arterial phase: Moderate enhancement — Portal phase: Lesions enhance similar to surrounding liver — Delayed phase: Lesions enhance similar to surrounding liver
DDX:
Complications: — Larger lesions are more prone to bleeding and rupture — Benign tumor with potential for malignant transformation into hepatocellular carcinoma
Treatment: Surgical resection if greater than 5 centimeters
Clinical: — Seen in older children and adolescents — Seen in young female with history of oral contraceptive pill use