A Pediatric Radiology textbook and Pediatric Radiology digital library
Heterotaxy Syndrome
Etiology: congenital
Asplenia: — Imaging: bilateral right sidedness with bilateral eparterial bronchus (bronchus is posterio-superior to pulmonary artery) and bilateral trilobed lungs — Clinical: severe cyanosis, severe congenital heart disease, susceptible to infection
Polysplenia: — Imaging: bilateral left sidedness with bilateral hyparterial bronchus (bronchus is anterio-inferior to pulmonary artery) and bilateral bilobed lungs — Clinical: less congenital heart disease, presents later, associated with biliary atresia