Heterotaxy Syndrome

• Etiology: congenital
• Asplenia:
  — Imaging: bilateral right sidedness with bilateral eparterial bronchus (bronchus is posterio-superior to pulmonary artery) and bilateral trilobed lungs
  — Clinical: severe cyanosis, severe congenital heart disease, susceptible to infection
• Polysplenia:
  — Imaging: bilateral left sidedness with bilateral hyparterial bronchus (bronchus is anterio-inferior to pulmonary artery) and bilateral bilobed lungs
  — Clinical: less congenital heart disease, presents later, associated with biliary atresia

Cases of Heterotaxy Syndrome