Hypoplastic Left Heart Syndrome

  • Etiology: left side obstructive lesion, spectrum of hypoplastic left atrium / mitral valve / left ventricle / aortic valve / proximal aorta
  • CXR: cardiomegaly, pulmonary venous congestion pattern – interstial prominence, Kerley lines, pulmonary edema
  • Clinical: one of few causes of failure in first 24 hours, corrected by 3 stage Norwood repair

Radiology Cases of Hypoplastic Left Heart Syndrome

CXR of hypoplastic left heart syndrome / HLHS
CXR AP shows increased pulmonary vascularity and cardiomegaly.