Pediatric Idiopathic Orbital Inflammation

  • Etiology: Idiopathic inflammatory condition that most commonly involves extraocular muscles and less commonly involves the uvea, sclera, lacrimal gland and retrobulbar soft tissue
  • Imaging: Enlargement of muscle belly of one or more extraocular muscles typically with involvement of tendinous insertions
  • DDX:
    — Orbital lymphoma which presents slowly and is usually bilateral
    — Thyroid associated orbitopathy which spares tendinous insertions of extraocular muscles and is usually painless
    — Orbital cellulitis that has subperiosteal abscess from adjacent cellulitis
    — Orbital rhabdomyosarcoma
  • Complications:
  • Treatment: Usually resolves rapidly with corticosteroid treatment
  • Clinical: Commonly presents with unilateral rapid-onset painful proptosis and diplopia

Radiology Cases of Idiopathic Orbital Inflammation

CT of idiopathic orbital inflammation
Axial (left) and coronal (right) CT with contrast of the orbits shows diffuse thickening of the muscle belly of the left lateral rectus muscle. No other inflammatory changes were seen in the orbits.