Kawasaki Disease

  • Etiology: medium vessel vasculitis causing strictures interposed by aneurysms, involves coronary arteries / aorta + secondary branches / pulmonary artery
  • Imaging: initially see lymphadenopathy + gallbladder hydrops, subsequently see coronary aneurysms in 1/3rd of patients (egg shell calcifications), aneurysms are variable in size + can be fusiform or saccular
  • MRI: vessel wall thickening and enhancement
  • Complications: coronary artery aneurysms, pericarditis, myocarditis, valvular disease
  • Clinical: 6 months old -> 4 years old

Radiology Cases of Kawasaki Disease

US of gallbladder hydrops in Kawasaki's disease