Pediatric Melorheostosis

  • Etiology: Mesenchymal dysplasia
  • Imaging Radiograph:
    — Changes not usually visible until late adolescence or early adulthood
    — Can be monostotic or polyostotic and tends to be monomelic
    — Predilection for limb long bones and hands and feet
    — Region of bone hyperostosis with dripping wax or flowing candle wax appearance that can be seen to flow across joints
  • DDX:
  • Complications: Long term can have disability from contractures
  • Treatment:
  • Clinical: Usually asymptomatic in children

Radiology Cases of Melorheostosis

Radiograph of melorheostosis
AP and oblique radiographs of the hand show a flame-shaped sclerotic lesion in the proximal aspect of the third metacarpal.