A Pediatric Radiology Textbook and Pediatric Radiology Digital Library
Mesoblastic Nephroma
Etiology: Hamartoma of kidney, classification has 3 types: — Classic: Non-aggressive, usually solid, no hemorrhagic or cystic or necrotic components — Cellular: More aggressive — Mixed:
Imaging: — Predominantly solid but may contain cystic components and therefore can be homogeneous or heterogenous — Variable enhancement as solid components may enhance due to nephron entrapment
Imaging US: Non-encapsulated large solid renal mass that may be difficult to separate from kidney
DDX:
Complications: 10% relapse – mostly cellular type
Treatment: Surgical
Clinical: — 5% of all renal tumors — Most common renal neoplasm in fetus and children less than 1 year old — Presentation Prenatal: Polyhydramnios, hydrops, pulmonary hypoplasia — Presentation Postnatal: Incidental mass, hypertension (renin – entrapped renal elements), hypercalcemia (parathormone), respiratory distress
Radiology Cases of Mesoblastic Nephroma
Radiology Cases of Mesoblastic Nephroma Classic Type
Transverse (above) and sagittal (below) US images shows an enlarged solid reniform shaped mass in the right renal fossa.
Radiology Cases of Mesoblastic Nephroma Cellular Type
Coronal CT with contrast of the abdomen (below) shows a solid mass with variable enhancement with cystic components within the right kidney. Axial CT (above) shows the cystic component of the mass extends to the midline. No claw sign is present. The left kidney is normal.
Surgery Cases of Mesoblastic Nephroma Classic Type
Surgical image shows an extremely large right renal tumor displacing the cecum into the left lower quadrant.
Gross Pathology Cases of Mesoblastic Nephroma Classic Type
Gross pathological image shows a large, round, solid renal mass after resection.Gross pathological image shows a light tan to yellow colored tumor mass situated within the lower pole of the kidney which has a fibrous, whorled cut section reminiscent of a leiomyoma.
Histopathology Cases of Mesoblastic Nephroma Classic Type
Histopathological image H&E stained section of a classic histology mesoblastic nephroma shows bundles of bland, spindle shaped cells infiltrating normal renal parenchyma. Glomeruli and tubules are not part of the tumor.