Pediatric Moya Moya Disease

  • Etiology: idiopathic
  • Imaging: occlusion of internal carotid terminus, reconstitution of M1/A1 via thalmoperforators (puff of smoke) and cortical collaterals
  • MRI: Failure to suppress sulcal CSF on FLAIR, sulcal enhancement, dilated perforators in diencephalon, T2 hypointense white matter under ischemic cortex
  • Clinical: presentation in childhood – seizure / TIA / ischemic stroke, presentation in adults – hemorrhagic stroke

Radiology Cases of Moya Moya Disease