Nephroblastomatosis

  • Etiology: forcal or multifocal fetal metanephric blastema tissue (nephrogenic rests) that persist after birth and which can develop into Wilms tumor
  • CT: low density
  • MRI: T1+T2 hypointense, if T2 hyperintense suspect Wilms tumor
  • Clinical: associated syndromes – Beckwith-Wiedemann, hemihypertrophy, Drash syndrome, sporadic aniridia, WAGR syndrome

Cases of Nephroblastomatosis