A Pediatric Radiology Textbook and Pediatric Radiology Digital Library
Osteopetrosis
Etiology: Dysfunctional osteoclasts leads to undertubulation of bones (Erlenmeyer flask deformity) and osteosclerosis
Imaging Radiograph: — Bone within bone — Thick skull — Bone is solid but brittle so see transverse fractures in bones
DDX:
Complications:
Treatment:
Clinical: Blindness with encroachment of optic foramina
Radiology Cases of Osteopetrosis
AP radiograph of the pelvis shows an osteosclerotic appearance to the bones with obliteration of the marrow spaces and a developing bone within bone appearance especially in the femurs.