Persistent Hyperplastic Primary Vitreous

  • Etiology: Failure of normal regression of embryonic hyaloid vascular system
  • Imaging:
    — Small globe
    — Unilateral or bilateral
    — Not calcified
    — Primary vitreous becomes condensed into narrow triangular retrolental vascular tuft of tissue (Cloquet’s canal)
  • DDX:
  • Complications:
  • Treatment:
  • Clinical: Leukocoria

Radiology Cases of Persistent Hyperplastic Primary Vitreous