- Etiology: heterozygous germline mutation in DICER1, mesenchymal and epithelial components resembling fetal lung
- Imaging: Type 1 is cystic / Type II is mixed cystic and solid / Type III is solid, can be multifocal, large in size, pleural effusion, mediastinal shift, lack of chest wall invasion, associated with spontaneous pneumothorax
- Clinical: most common primary malignancy of lungs in childhood, extremely rare, < 2 years old
Radiology Cases of Pleuropulmonary Blastoma
