Pulmonary Atresia

  • Etiology: Congenital
  • Imaging: Right to left shunt and right ventricular outflow obstruction leads to cyanosis and decreased pulmonary blood flow
  • Imaging CXR: Cardiomegaly due to right atrial enlargement with decreased pulmonary blood flow
  • DDX:
  • Complications:
  • Treatment:
  • Clinical:

Radiology Cases of Pulmonary Atresia

CXR of pulmonary atresia with intact ventricular septum
CXR AP shows decreased pulmonary vascularity and mild cardiomegaly.
CXR of pulmonary atresia
CXR AP shows cardiomegaly and relatively decreased pulmonary vascularity.