Pulmonary Lymphangiectasia

  • Etiology: Congenital grossly dilated lymphatic vessels throughout the lung due to narrowing or occlusion of the thoracic duct
  • Imaging:
    — Perihilar infiltrates due to interstitial and interlobular septal thickening
    — Chylothorax
  • DDX: Pulmonary edema
  • Complications:
  • Treatment:
  • Clinical:

Radiology Cases of Pulmonary Lymphangiectasia

CXR of pulmonary lymphangiectasia
CXR AP and lateral shows mild cardiomegaly and diffuse interstitial infiltrates with no evidence of pleural effusions.

CXR and CT of pediatric pulmonary lymphangiectasia
CXR AP (above) shows diffuse interstitial infiltrates with no evidence of pleural effusions. Coronal CT without contrast of the lung (below) shows diffuse interstitial and interlobular septal thickening throughout the lungs.