Pyriform Aperture Stenosis

• Etiology: Maldevelopment of inferior maxilla due to early fusion and hypertrophy of medial nasal processes
• Imaging CT:
  — Axial images should be reformatted to be parallel to the plane of the anterior hard palate
  — Narrowing of pyriform aperture
  — Stenosis results in loss of normal pyramidal shape of nasal fossa
  — Central megaincisor is frequently seen
• DDX:
• Complications:
• Treatment:
• Clinical:
  — Presents with failure to pass nasogastric tube
  — May be isolated or a component of other mid-facial maldevelopment or accompanied by holoprosencephaly

Radiology Cases of Pyriform Aperture Stenosis