Pediatric Scleroderma

  • Etiology: Autoimmune connective tissue disorder characterized by multisystem fibrosis and soft tissue calcification
  • Imaging Radiograph:
    — Articular findings: Acro-osteolysis, periarticular osteopenia, joint space narrowing, joint erosions, resorption of first carpometacarpal joint with radial subluxation, pencil-in-cup deformity
    — Extra-articular findings: Subcutaneous and periarticular calcification, soft tissue atrophy especially at fingertips, flexion contractures
  • DDX: Rheumatoid arthritis
  • Complications:
  • Treatment:
  • Clinical:

Radiology Cases of Scleroderma

Hand radiograph of scleroderma
AP radiograph of the hand shows acroosteolysis of the second and third distal phalanges and faint soft tissue calcifications at the tips of the first, second and third distal phalanges.