Urethral Atresia

Etiology: Congenital absence of urethra
Imaging Prenatal US: Anhydramnios or oligohydramnios
Imaging:
— Bilateral hydroureteronephrosis and dilated bladder
— Cystic renal dysplasia
— Urinoma or urine ascites
DDX: Posterior urethral valves
Complications: Incompatible with life
Treatment: Intra uterine vesico-amniotic shunt
Clinical: Oligohydramnios

Radiology Cases of Urethral Atresia

AXR of urethral atresia — Postmortem CXR and AXR shows an extremely distended abdomen due to bilateral abdominal masses resulting in a small thorax. An umbilical catheter fragment is also present.

Clinical Cases of Urethral Atresia

Clinical image of Potter's facies due to urethral atresia — Post-mortem gross pathological image shows Potter’s facies – a flattened face and low set ears – and a small thorax with pulmonary hypoplasia and large abdomen.

Gross Pathology Cases of Urethral Atresia

Gross pathology image of cystic renal dysplasia and a trabeculated bladder due to urethral atresia — Post-mortem gross pathological image shows bilaterally enlarged kidneys containing multiple large cysts and a trabeculated bladder inferior to the right kidney.

Gross pathology image of cystic renal dysplasia and a trabeculated bladder due to urethral atresia — Post-mortem gross pathological image shows enlarged kidneys containing multiple large cysts bilaterally, left hydroureter (which was also present on the right) and a thick walled and trabeculated bladder.

Gross pathology image of cystic renal dysplasia due to urethral atresia — Gross pathological sectioned image shows an enlarged kidney which contains multiple large cysts.