Wolman Disease

Etiology: Lysosomal acid lipase deficiency which results in accumulation of lipid esters in liver, spleen, lymph nodes, adrenal cortex, and small bowel which can lead to malabsorption and thus malnutrition
Imaging AXR: Bilateral diffuse calcification in enlarged adrenal glands
DDX:
Complications:
Treatment:
Clinical:

Radiology Cases of Wolman Disease

AXR AP and lateral shows bilateral diffuse calcification in enlarged adrenal glands.