School ager with cafe-au-lait spots

Musculoskeletal, Neurological
CXR and CT of plexiform neurofibroma in neurofibromatois type 1
CXR PA shows a large soft tissue mass in the apex of the right lung which causes thinning of the right 1st-5th ribs posteriorly. CT without contrast of the chest shows multiple small nodules throughout the soft tissues of the chest wall.

The diagnosis was multiple plexiform neurofibromas in a patient with neurofibromatosis type 1.

Published