School ager with large and rapidly enlarging soft tissue mass involving his right arm and chest

Surgical-Pathological-Clinical
Surgery image of malignant peripheral nerve sheath tumor
Surgical image through a right thoracotomy shows a large mass originating in the apex of the right chest. Normal lung can be seen in the upper right corner of the incision.

The diagnosis was malignant peripheral nerve sheath tumor in a patient with multiple plexiform neurofibromas who has neurofibromatosis Type 1.

Published